Diencephalic Syndrome, autoimmune?
eMedicine Specialties > Dermatology > PEDIATRIC DISEASES
eMedicine - Lawrence-Seip Syndrome : Article by Camila K Janniger
Autoimmune disorders also may be common, including Coombs-positive hemolytic anemia and ... Diencephalic syndrome of infancy Congenital muscular dystrophy ...
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Acquired Lawrence-Seip syndrome - Generalized lipodystrophy often is preceded by an illness and, in many instances, an infection. The fat loss becomes apparent either focally or diffusely, usually beginning in adolescence or early adult life.
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- Most of the features of the congenital form may occur, but in the acquired form, neurologic, cardiac, and renal abnormalities usually are absent.
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- Bone age is normal and genital hypertrophy is absent.
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- AN to varying degrees probably is a constant finding in acquired and congenital forms.
- Autoimmune disorders also may be common, including Coombs-positive hemolytic anemia and chronic nephritis; however, great variability exists in the immunologic abnormalities in patients with the acquired form. Patients with the acquired form of Lawrence-Seip syndrome also are prone to infection.
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Prone to Infection?
If they think so because of high white blood cell counts,
it may just be another sign of the AIHA or of NHL
Why?
